Arrhythmogenic right ventricular dysplasia is a rare entity and a significant cause of sudden death especially in the Italian population and athletes. The familial form is uncommon especially in the Afro-Caribbean population.
Congenital paroxysmal atrial fibrillation in infants is a rare occurrence requiring a high index of suspicion. The majority have a pre-excitation syndrome which may be concealed. It may be associated with specific structural congenital cardiac lesions. This index case had only paroxysmal atrial tachyarrhythmia with no predisposing condition that subsided spontaneously and is the first case documented in an Afro-Caribbean infant.